What are Desmoplastic Small Round Cell Tumors?
Desmoplastic Small Round Cell Tumor is a rare, aggressive cancer that grows in the abdomen and pelvic area. It has the propensity to spread to the peritoneal cavity and form multiple masses in it. The tumor affects young men and adolescents. In the case of women, this tumor is rarely detected and it may be confused with ovarian cancer in some cases.
Common Symptoms:
1) Abdominal pain
2) Abdominal lumps
3) Symptoms of intestinal obstruction
The tumor may be aggressive and widespread but cytoreductive surgery and HIPEC has shown to almost double the survival in such patients. CRS and HIPEC for desmoplastic small round cell tumors may be combined with systemic systemic chemotherapy before or after the surgery.